|
KMID : 0882419950490020293
|
|
Korean Journal of Medicine
1995 Volume.49 No. 2 p.293 ~ p.297
|
|
|
A Case of Severe Hyponatremia during Acute Attack of Porphyria
|
|
정철원
전은실/정우경/김원석/조종태/안규리/한진석/김성권/이정상
|
|
|
Abstract
|
|
|
Hepatic porphyria shows impaired heme biosynthesis predominantly in the liver and usually presents with abdominal pain, vomiting, photossensitivity and neurologic abnormalities and sometimes with hyponatremia accompanied by syndrome of
inappropriate
antidiuretic hormone secretion(SIADH).
We report a case seemed to be a hereditaty coproporphyria presenting with acute abdominal pain and vomiting. She had severe hyponatremia with the feature of SIADH and peripheral neuropathy which was provoked by the ingestion of alcohol, poor oral
intake
and by the administration of imipramin. She was thought to have hereditary coproporphyria by the clinical feature, stool porphyrin and quantitation of the 24 hour urine δ-aminolevulinic acid, porpho-bilinogen and porphyrins. Supportive treatment
with
NaCl in fusion and propranolol resulted in symptomatic recovery and she was discharged after education of precipitating factors.
|
|
|
KEYWORD
|
|
|
|
|
|
FullTexts / Linksout information
|
|
|
|
|
Listed journal information
|
|
  
|